- Case Report
- A Case of Congenital Dyserythropoietic Anemia, Type II
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Won Kyung Yang, Jung Wan Yoo, Hyung Goo Cho, Dong Chul Park, In Sung Lee, Won Yong Lee
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Clin Exp Pediatr. 1994;37(1):99-103. Published online January 15, 1994
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Congenital dyserythropoietic anemia Type II (herditary erythroblatic multinuclearity with positive acidfied serum test;HEMPAS) is characterized by binuclearity, multinuclearity, pluripolar mitoses, karyorrhexis of normoblasts, and the presence of abnormla antigens on the red cells.
We experienced a case of HEMPAS in a 2 month old girl patient who had an intermittent fever, abdominal distention with palpable liver & spleen, and generalized jaundice.
The... |
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